Huntington’s chorea is a neurodegenerative disease of autosomal dominant inheritance and presents with motor findings such as dystonia, psychiatric disorder, and progressive dementia. Nursing care is of crucial importance in cases with Huntington’s chorea because the disease has profound effects on the biological, physiological, socio-cultural, and economic domains. Thus, nurses who provide care for patients with Huntington’s chorea should know about the disease and its diagnosis and treatment and should be able to monitor complications and side effects related to care and treatment and plan and implement care interventions aimed at alleviating such complications and side effects. In this article, nursing care in patients with Huntington’s chorea was examined according to the phases of the nursing process, which are diagnosis, planning-nursing interventions, implementation, and assessment. In addition, it was aimed to draw attention to the importance of problems encountered by these patients and of nursing interventions.